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Turner SyndromePhase 4NCT06570460

Long Term Effects of Oral Versus Transdermal Estrogen Replacement Therapy in Turner Syndrome

A Phase 4 study testing 17-beta estradiol in people with Turner Syndrome and Hypogonadism; Ovarian, run by Aarhus University Hospital at 1 site in Denmark.

Recruiting

Looking for participants now. Contact the study team or a site below to ask about taking part.

Sites and contacts
Official record
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Trial summary

This 14-month, phase IV, randomized controlled crossover trial aims to compare the effects of oral versus transdermal estrogen replacement therapy (ERT) in women with Turner syndrome (TS). Read more about this study

Who is it for?
Ages 18 to 50 years, women onlyHealthy volunteers can take part
What is being tested?
17-beta estradiol
Type of treatment
Pill or oral medicine
Could I receive a placebo?
No, everyone receives an active treatment
How many people
50 participants
Where
1 siteDenmark
Study dates
29 Nov 2021to 31 Dec 2026
Phase
Phase 4
Are there results?
Not yet: the study is under way

Key requirements

Who can take part, as listed by the sponsor. Only the study team can confirm whether you are eligible, so take this list to your doctor.

  • Ages 18 to 50 years
  • Women only
  • Healthy volunteers accepted
  • Adult

Who may be able to join

  • For participants with TS:
  • Diagnosis of TS regardless of karyotype
  • Age 18-50 years
  • Already receiving estrogen treatment
  • For healthy controls:
  • Female
Show all 11Show fewer
  • Age 18-50 years
  • Previously healthy
  • Not receiving any medication
  • Not using any form of contraceptive pills
  • No mental or psychiatric disorders

Who cannot join

  • Active systemic chronic diseases
  • Known or suspected breast cancer
  • Known or suspected estradiol-dependent tumors (endometrial cancer or similar)
  • Untreated endometrial hyperplasia
  • Current or previous venous thromboembolism
  • Acute or previous liver disease where liver enzymes are still elevated by a factor 3 or more
Show all 9Show fewer
  • Known hypersensitivity to the medications used
  • Pregnancy
  • Menopause (for the control group only)

Trial locations and contacts

1 site in 1 country. Contact the study team or a site near you to ask about taking part.

Camilla M Balle, Ph.d.-student contact

40769623 ext. 0045

camibl@clin.au.dk

Claus H Gravholt, Professor contact

78455470 ext. 0045

claus.gravholt@clin.au.dk

Denmark1 site, 1 recruiting
  • Department of Endocrinology and Internal Medicine, Aarhus University Hospital

    Aarhus, Aarhus N, 8200

    Camilla M Balle, Ph.d.-student, 40769623, camibl@clin.au.dk

    Recruiting

Other trials in Denmark

About this study

Official title: Long Term Effects of Oral Versus Transdermal Estrogen Replacement Therapy in Turner Syndrome - A Randomized Trial

This 14-month, phase IV, randomized controlled crossover trial aims to compare the effects of oral versus transdermal estrogen replacement therapy (ERT) in women with Turner syndrome (TS). The study's objectives are to clarify endocrine, metabolic, cardiovascular, and thromboembolic risk factors in TS after a wash-out period without estrogen (E2) treatment; compare the effects of oral versus transdermal (TD) ERT regimens; and examine the long-term effects of E2 administration via these two routes. The study involves 50 TS women aged 18-50 years and 50 control participants. TS participants are randomized to receive either oral or TD ERT for six months, followed by crossover to the alternate treatment for another six months. Prior to randomization, any existing ERT will be discontinued for a 1-month washout period. A second 1-month washout period will occur between the two 6-month treatment phases. Laboratory analyses and clinical investigations are performed after the first wash-out period, after the first six months of treatment, and after the last six months of treatment. We anticipate that this study may provide a basis for new and improved recommendations for sex hormone replacement therapy in TS.

Read the detailed description

OBJECTIVES

  1. Clarify endocrine, metabolic, cardiovascular and thromboembolic risk factors in Turner syndrome (TS) after a wash out period
  2. Compare the effects of oral versus transdermal (TD) estrogen replacement therapy (ERT) in women with Turner syndrome
  3. Examine long term effects of ERT via the two routes on endocrine, metabolic, cardiovascular, physiologic and thromboembolic risk endpoints

BACKGROUND Turner syndrome (TS) is a rare genetic condition affecting approximately 1 in 2,000 female births. A hallmark of TS is ovarian dysgenesis, leading to hypogonadism, premature ovarian failure, and infertility. Consequently, estrogen replacement therapy (ERT) is typically initiated around age 11-12 to induce puberty and continued until the average age of menopause (50-55 years), aiming for at least 42 years of adequate estrogen exposure.

Hypogonadism in TS is associated with various health complications. Importantly, estradiol (E2) replacement may mitigate these risks. Estrogen deficiency in TS affects cardiovascular health (hypertension, congenital cardiac disease, altered lipid profiles), metabolic function (diabetes, thyroid dysfunction, hepatic disorders, kidney disease, skeletal abnormalities), and is linked to neurocognitive and social challenges.

E2 can be administered orally or transdermally (TD), but it remains unclear whether either route offers specific advantages. There is ongoing debate regarding a potential increased thromboembolic risk in TS patients treated with oral E2. Epidemiological studies in postmenopausal women have reported an elevated thromboembolic risk associated with oral estrogen treatment, but to a lesser extent with TD administration. However, extrapolating data from postmenopausal women to TS patients is inappropriate, as women with TS receive estrogen as replacement therapy due to inadequate endogenous production. Furthermore, limited knowledge exists regarding the side effects of oral versus TD estrogen replacement therapy for TS patients.

MATERIALS AND METHODS

Study group:

Women aged 18-50 years with TS recruited primarily from the Department of Endocrinology at Aarhus University Hospital (n=50); 300 patients with TS are currently followed in the outpatient clinic. The investigators also have the opportunity to recruit from the Turner Association in Denmark, and finally the investigators do have contact with other outpatient clinics with TS patients in Denmark from where the investigators have previously recruited TS patients.

An age-matched control group of healthy women is included by advertisement (n=50).

Inclusion criteria:

For participants with TS:

  • Diagnosis of TS regardless of karyotype
  • Age 18-50 years
  • Already receiving estrogen treatment

For healthy controls:

  • Female
  • Age 18-50 years
  • Previously healthy
  • Not receiving any medication
  • Not using any form of contraceptive pills
  • No mental or psychiatric disorders

Exclusion criteria:

  • Active systemic chronic diseases
  • Known or suspected breast cancer
  • Known or suspected estradiol-dependent tumors (endometrial cancer or similar)
  • Untreated endometrial hyperplasia
  • Current or previous venous thromboembolism
  • Acute or previous liver disease where liver enzymes are still elevated by a factor 3 or more
  • Known hypersensitivity to the medications used
  • Pregnancy
  • Menopause (for the control group only)

Design:

A 14-month, phase IV, randomized controlled crossover study involving women with Turner Syndrome (TS) (n=50) and healthy, age-matched controls (n=50). TS participants are randomized to receive either oral or TD ERT for six months, followed by crossover to the alternate treatment for another six months. Prior to randomization, any existing ERT will be discontinued for a 1-month washout period. A second 1-month washout period will occur between the two 6-month treatment phases. Healthy controls will not receive any treatment. They will undergo a single set of assessments for comparison.

Laboratory analyses and clinical investigations will be conducted at the Department of Endocrinology and the associated Medical Research Unit at Aarhus University Hospital. These will include blood and urine sample collection, as well as specific clinical investigations. At baseline, both TS patients and healthy controls will undergo these assessments. Only TS patients will undergo follow-up assesments.

Clinical investigations:

  • Insulin sensitivity assessment
  • 24-hour blood pressure monitoring
  • DEXA scan (Dual-Energy X-ray Absorptiometry)
  • Bioelectrical impedance analysis (Multiplate)
  • Comprehensive clinical examination
  • Quality of life assessments using questionnaires
  • SphygmoCor analysis
  • VO2 max test using a stationary bike
  • MRI of the thigh muscles to measure muscle cross-sectional area (CSA) and intramuscular fat content
  • Isometric muscle strength testing and functional testing

STATISTICS Data will be summarized by treatment group and assessment time point. The investigators will use a mixed model with repeated measures analysis of variance (ANOVA) to compare the mean changes in each of the study variables between treatments over time. When appropriate, transformations or nonparametric methods will be used. All tests are two-tailed with a 5% level of significance. Data are presented as mean ± SE or median with CI for metrics not normally distributed.

PERSPECTIVES Patients with TS undergo hormone replacement therapy from puberty to menopause, spanning more than 40 years of treatment. To date, only two experimental studies have compared oral and TD ERT in TS, focusing solely on metabolic parameters and finding no differences between the two regimens. If the investigators' hypotheses are correct and if the side effects, including increased thromboembolic risk, are higher with oral than TD ERT, this project could be crucial for optimizing treatment, improving quality of life, and reducing morbidity and mortality in TS. The investigators aim for this study to provide a basis for new and improved national and international recommendations for ERT in TS patients and to contribute new knowledge about hormonal treatment for the general population as well.

Being tested
17-beta estradiol
Keywords
Turner syndrome, Hormone replacement therapy, Estrogen replacement therapy, Estrogen treatment, Long term side effects
Medical subject headings
Turner Syndrome, Hypogonadism

What participants receive

What participants receive. In a randomised study each person is assigned to one group by chance.

  • 17-beta estradiolDrug

    Also called Estrofem

    Treatment with orally administered estrogen for 6 months

  • 17-beta estradiolDrug

    Also called Divigel

    Treatment with transdermally administered estrogen for 6 months

Study groups in NCT06570460
Study groupRoleWhat they receive
Oral estrogen treatmentActive comparatorTurner syndrome patients receiving oral estrogen treatment (Estrofem®)
Receives: Drug: 17-beta estradiol
Transdermal estrogen treatmentActive comparatorTurner syndrome patients receiving transdermal estrogen treatment (Divigel)
Receives: Drug: 17-beta estradiol
ControlsNo interventionHealthy age-matched controls receiving no treatment

What is being measured

The primary outcome is the main question the study is designed to answer.

  1. Blood test values

    Changes in blood test values of follicle stimulating hormone and luthenizing hormone from baseline

    Measured: After 1 month of wash-out, 6 months of oral and six months of transdermal treatment

  2. Blood test values

    Changes in blood test values of estradiol from baseline

    Measured: After 1 month of wash-out, 6 months of oral and six months of transdermal treatment

  3. Dual energy X-ray absorptiometry

    Changes in body composition and bone mineral density

    Measured: After 6 months of oral and six months of transdermal treatment

  4. Cardiovascular status

    Changes in 24-hour blood pressure measurements

    Measured: After 6 months of oral and six months of transdermal treatment

  5. Cardiovascular status

    Changes in arterial stiffness measured by SphygmoCor

    Measured: After 6 months of oral and six months of transdermal treatment

  6. Muscle quality (quadriceps femoris)

    MR scan of both quadriceps measuring muscle cross-sectional area (CSA) and fat content of the muscle. Maximal isometric muscle strength of both quadriceps (functional muscle tests). Muscle quality = maximum quadriceps strength measured in nM/muscle CSA.

    Measured: After 6 months of oral and six months of transdermal treatment

  7. Functional muscle tests

    Changes in maximal jumping height

    Measured: After 6 months of oral and six months of transdermal treatment

  8. Isometric muscle tests

    Changes in maximal isometric hand strength

    Measured: After 6 months of oral and six months of transdermal treatment

  9. Maximal oxygen uptake test (VO2 max)

    Changes in maximal oxygen uptake

    Measured: After 6 months of oral and six months of transdermal treatment

Secondary outcomes (3)
  1. Self-reported health-related quality of life and functioning (SF-36)

    The Short Form 36 Health Survey is a self-reported quality of life questionnaire consisting of eight scaled scores. Each scale is transformed directly into a 0-100 scale, where a lower score indicates greater difficulty.

    Measured: After 6 months of oral and six months of transdermal treatment

  2. Self-reported quality of life (WHOQoL-Bref)

    The WHOQoL-Bref is a questionnaire where the participant's answers to 26 questions are used to create an overall quality of life profile. This profile includes scores for each dimension of the questionnaire: physical health, mental health, social relationships, and the participant's environment.

    Measured: After 6 months of oral and six months of transdermal treatment

  3. Subjective medication assesment

    Subjective assesment of the medication after 6 months of use

    Measured: After 6 months of oral and six months of transdermal treatment

Timeline

From the start of the study to its completion; the mark is today. Estimated dates are the sponsor’s plan.

  1. First posted26 Aug 2024
  2. Study start29 Nov 2021
  3. Primary completion31 Dec 2026 (estimated)
  4. Study completion31 Dec 2026 (estimated)

Resources

More details

For doctors and researchers: how the study is designed, who runs it, and its registry IDs.

Study design
Study type
Interventional
Phase
Phase 4
Primary purpose
Treatment
Allocation
Randomised
Intervention model
Crossover
Model description
A randomized controlled trial
Masking
None (open label)
Enrolment
50 participants (estimated)
IDs, dates and publications
ClinicalTrials.gov ID
NCT06570460
Sponsor's protocol ID
AU2019TS2
Status last verified
Jul 2024
First submitted
4 Dec 2019
Last updated
26 Aug 2024
Results posted
No
Data monitoring committee
Yes
FDA-regulated drug
No
FDA-regulated device
No
Individual data sharing
No

Publications

  • Stochholm K, Juul S, Juel K, Naeraa RW, Gravholt CH. Prevalence, incidence, diagnostic delay, and mortality in Turner syndrome. J Clin Endocrinol Metab. 2006 Oct;91(10):3897-902. doi: 10.1210/jc.2006-0558. Epub 2006 Jul 18.

    PubMed 16849410
  • Gravholt CH, Andersen NH, Conway GS, Dekkers OM, Geffner ME, Klein KO, Lin AE, Mauras N, Quigley CA, Rubin K, Sandberg DE, Sas TCJ, Silberbach M, Soderstrom-Anttila V, Stochholm K, van Alfen-van derVelden JA, Woelfle J, Backeljauw PF; International Turner Syndrome Consensus Group. Clinical practice guidelines for the care of girls and women with Turner syndrome: proceedings from the 2016 Cincinnati International Turner Syndrome Meeting. Eur J Endocrinol. 2017 Sep;177(3):G1-G70. doi: 10.1530/EJE-17-0430.

    PubMed 28705803
  • Hjerrild BE, Mortensen KH, Gravholt CH. Turner syndrome and clinical treatment. Br Med Bull. 2008;86:77-93. doi: 10.1093/bmb/ldn015. Epub 2008 Apr 9.

    PubMed 18400842
  • Gravholt CH, Landin-Wilhelmsen K, Stochholm K, Hjerrild BE, Ledet T, Djurhuus CB, Sylven L, Baandrup U, Kristensen BO, Christiansen JS. Clinical and epidemiological description of aortic dissection in Turner's syndrome. Cardiol Young. 2006 Oct;16(5):430-6. doi: 10.1017/S1047951106000928.

    PubMed 16984695
  • Mortensen KH, Andersen NH, Hjerrild BE, Horlyck A, Stochholm K, Hojbjerg Gravholt C. Carotid intima-media thickness is increased in Turner syndrome: multifactorial pathogenesis depending on age, blood pressure, cholesterol and oestrogen treatment. Clin Endocrinol (Oxf). 2012 Dec;77(6):844-51. doi: 10.1111/j.1365-2265.2012.04337.x.

    PubMed 22233516
  • Mauger C, Lancelot C, Roy A, Coutant R, Cantisano N, Le Gall D. Executive Functions in Children and Adolescents with Turner Syndrome: A Systematic Review and Meta-Analysis. Neuropsychol Rev. 2018 Jun;28(2):188-215. doi: 10.1007/s11065-018-9372-x. Epub 2018 Apr 27.

    PubMed 29704077
  • Hansen M. Female hormones: do they influence muscle and tendon protein metabolism? Proc Nutr Soc. 2018 Feb;77(1):32-41. doi: 10.1017/S0029665117001951. Epub 2017 Aug 29.

    PubMed 28847313
  • Greising SM, Baltgalvis KA, Lowe DA, Warren GL. Hormone therapy and skeletal muscle strength: a meta-analysis. J Gerontol A Biol Sci Med Sci. 2009 Oct;64(10):1071-81. doi: 10.1093/gerona/glp082. Epub 2009 Jun 26.

    PubMed 19561145
  • Canonico M, Plu-Bureau G, Lowe GD, Scarabin PY. Hormone replacement therapy and risk of venous thromboembolism in postmenopausal women: systematic review and meta-analysis. BMJ. 2008 May 31;336(7655):1227-31. doi: 10.1136/bmj.39555.441944.BE. Epub 2008 May 20.

    PubMed 18495631
  • Renoux C, Dell'aniello S, Garbe E, Suissa S. Transdermal and oral hormone replacement therapy and the risk of stroke: a nested case-control study. BMJ. 2010 Jun 3;340:c2519. doi: 10.1136/bmj.c2519.

    PubMed 20525678
  • Sweetland S, Beral V, Balkwill A, Liu B, Benson VS, Canonico M, Green J, Reeves GK; Million Women Study Collaborators. Venous thromboembolism risk in relation to use of different types of postmenopausal hormone therapy in a large prospective study. J Thromb Haemost. 2012 Nov;10(11):2277-86. doi: 10.1111/j.1538-7836.2012.04919.x.

    PubMed 22963114
  • Gravholt CH, Naeraa RW, Fisker S, Christiansen JS. Body composition and physical fitness are major determinants of the growth hormone-insulin-like growth factor axis aberrations in adult Turner's syndrome, with important modulations by treatment with 17 beta-estradiol. J Clin Endocrinol Metab. 1997 Aug;82(8):2570-7. doi: 10.1210/jcem.82.8.4127.

    PubMed 9253336
  • Taboada M, Santen R, Lima J, Hossain J, Singh R, Klein KO, Mauras N. Pharmacokinetics and pharmacodynamics of oral and transdermal 17beta estradiol in girls with Turner syndrome. J Clin Endocrinol Metab. 2011 Nov;96(11):3502-10. doi: 10.1210/jc.2011-1449. Epub 2011 Aug 31.

    PubMed 21880799
  • Torres-Santiago L, Mericq V, Taboada M, Unanue N, Klein KO, Singh R, Hossain J, Santen RJ, Ross JL, Mauras N. Metabolic effects of oral versus transdermal 17beta-estradiol (E(2)): a randomized clinical trial in girls with Turner syndrome. J Clin Endocrinol Metab. 2013 Jul;98(7):2716-24. doi: 10.1210/jc.2012-4243. Epub 2013 May 15.

    PubMed 23678038
  • Gravholt CH, Naeraa RW, Nyholm B, Gerdes LU, Christiansen E, Schmitz O, Christiansen JS. Glucose metabolism, lipid metabolism, and cardiovascular risk factors in adult Turner's syndrome. The impact of sex hormone replacement. Diabetes Care. 1998 Jul;21(7):1062-70. doi: 10.2337/diacare.21.7.1062.

    PubMed 9653596

Questions about this trial

What is this clinical trial studying?

A Phase 4 study testing 17-beta estradiol in people with Turner Syndrome and Hypogonadism; Ovarian, run by Aarhus University Hospital at 1 site in Denmark.

The full registered description is in the About this study section and the official record.

Who may be eligible to take part?

The sponsor lists 11 inclusion and 9 exclusion criteria. Eligibility is decided by the study team after screening, so read the full criteria and contact a listed site.

Is this clinical trial currently recruiting?

The record says: looking for participants now, as of the sponsor's last update on 26 Aug 2024. Status can change between updates, so confirm with the study contact before making plans.

Where is the study taking place?

The record lists 1 site in Denmark. Whether a site is taking part right now should be confirmed with that site. See every site.

What are the possible benefits and risks?

They depend on the study and the treatment, and no study can promise a benefit. The study team explains the known risks during informed consent, before anyone joins; the record itself does not list them.

What does this phase mean?

Phase 4 studies take place after a treatment is approved, to learn more about its long-term benefits and risks in everyday use.

Not every study follows the same path, and some studies (observational studies, device studies) have no phase.

Are results available for this study?

This study is still under way. Results are not available in the source record yet.

How can a doctor refer a patient or contact the research team?

Contact Camilla M Balle, Ph.d.-student (40769623 ext. 0045, camibl@clin.au.dk), or a site near the patient. AzTrials does not enrol participants or take referrals.

What does the primary outcome measure?

Blood test values (time frame: After 1 month of wash-out, 6 months of oral and six months of transdermal treatment). The study lists 9 primary outcomes in all. It is what the study was designed to measure, not a finding.

Where can I read the original study information?

On the ClinicalTrials.gov record for NCT06570460, which also lists 18 linked publications.

Does a listing mean the treatment is approved or proven to work?

No. A listing means the study is registered. It does not show that the treatment is safe, works, or is approved by a regulator.

How often is this information updated?

AzTrials copies changed records from ClinicalTrials.gov every night and reloads the whole registry every week. The sponsor last updated this record on 26 Aug 2024.

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