Hemophilia BPhase 1/2NCT02396342
Trial of AAV5-hFIX in Severe or Moderately Severe Hemophilia B
A Phase 1/2 study testing AAV5-hFIX in people with Hemophilia B, run by CSL Behring at 7 sites in 3 countries.
Trial summary
This study evaluates how safe gene therapy treatment with AAV5-hFIX is in adult patients with severe or moderately severe hemophilia B and severe bleeding type. Read more about this study
- Who is it for?
- Ages 18 years and older, men only
- Conditions the study is for
- Hemophilia B
- What is being tested?
- AAV5-hFIX
- Type of treatment
- Injection or infusion
- Could I receive a placebo?
- No, everyone receives an active treatment
- How many people
- 10 participants
- Where
- 7 sitesin 3 countries
- Study dates
- 10 Jun 2015to 15 Apr 2021
- Phase
- Phase 1/2
- Are there results?
- Yes, posted in the registrySummary in the doctors' view
Key requirements
Who can take part, as listed by the sponsor. Only the study team can confirm whether you are eligible, so take this list to your doctor.
- Ages 18 years and older
- Men only
- No healthy volunteers
- Adult, Older adult
Who may be able to join
- Male
- Age ≥ 18 years
- Patients with congenital hemophilia B classified as one of the following:
- Known severe FIX deficiency with plasma FIX activity level < 1% and a severe bleeding phenotype defined by one of the following:
- Currently on prophylactic FIX replacement therapy for a history of bleeding
- Currently on on-demand therapy with a current or past history of frequent bleeding defined as four or more bleeding episodes in the last 12 months or chronic hemophilic arthropathy (pain, joint destruction, and loss of range of motion) in one or more joints
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- Known moderately severe FIX deficiency with plasma FIX activity level between ≥ 1% and ≤ 2% and a severe bleeding phenotype defined by one of the following:
- Currently on prophylactic FIX replacement therapy for a history of bleeding
- Currently on on-demand therapy with a current or past history of frequent bleeding defined as four or more bleeding episodes in the last 12 months or chronic hemophilic arthropathy (pain, joint destruction, and loss of range of motion) in one or more joints
- More than 150 previous exposure days of treatment with FIX protein.
- Acceptance to use a condom during sexual intercourse in the period from Investigational Medicinal Product (IMP) administration until AAV5 has been cleared from semen, as evidenced by the central laboratory from negative analysis results for at least 3 consecutively collected semen samples (this criterion is applicable also for subjects who are surgically sterilized)
- Following receipt of verbal and written information about the trial, the subject has provided signed informed consent before any trial related activity is carried out.
Who cannot join
- History of FIX inhibitors measured to be ≥ 0.6 Bethesda Units (BU)/mL
- FIX inhibitors ≥ 0.6 BU/mL at Visit 1 (measured by the local laboratory)
- Neutralizing antibodies against AAV5 at Visit 1 (measured by the central laboratory)
- Visit 1 laboratory values (measured by the central laboratory):
- alanine aminotransferase > 2 times upper normal limit
- aspartate aminotransferase > 2 times upper normal limit
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- total bilirubin > 2 times upper normal limit
- alkaline phosphatase > 2 times upper normal limit
- creatinine > 1.5 times upper normal limit
- Positive HIV serological test at Visit 1, not controlled with anti-viral therapy as shown by cluster of differentiation 4+ counts ≤ 200 per μL or by a viral load of >200 copies per mL (measured by the central laboratory)
- Active infection with Hepatitis B or C virus as reflected by Hepatitis B Surface Antigen (HBsAg), Hepatitis B extracellular Antigen (HBeAg), Hepatitis B Virus DeoxyriboNucleic Acid (HBV DNA) or Hepatitis C Virus RiboNucleic Acid (HCV RNA) positivity, respectively, at Visit 1 (measured by the central laboratory).
- History of Hepatitis B or C exposure, currently controlled by antiviral therapy
- Any coagulation disorder other than hemophilia B
- Thrombocytopenia, defined as a platelet count below 50 × 10E9 / L, at Visit 1 (measured by the central laboratory)
- Body mass index < 16 or ≥ 35 kg/m2
- Planned surgery for the initial 6 months after IMP administration in this trial
- Previous arterial or venous thrombotic event (e.g. acute myocardial infarction, cerebrovascular disease and venous thrombosis)
- Active severe infection or any other significant concurrent, uncontrolled medical condition including, but not limited to, renal, hepatic, haematological, gastrointestinal, endocrine, pulmonary, neurological, cerebral or psychiatric disease, alcoholism, drug dependency or any other psychological disorder evaluated by the investigator to interfere with adherence to the protocol procedures or with the degree of tolerance to the IMP
- Known significant medical condition including disseminated intravascular coagulation, fibrinolysis and liver fibrosis which, in the opinion of the investigator, may confound, contraindicate or limit the interpretation of either safety or efficacy data
- Known history of an allergic reaction or anaphylaxis to FIX products
- Known uncontrolled allergic conditions or allergy/hypersensitivity to any component of the IMP excipients
- Previous gene therapy treatment and/or previous participation in a gene therapy clinical trial
- Receipt of an experimental agent within 60 days prior to Visit 1
- Current participation or anticipated participation within one year after IMP administration in this trial in any other interventional clinical trial involving drugs or devices.
Trial locations and contacts
7 sites in 3 countries.
7 sites in 3 countries
Netherlands4 sites
uniQure Investigative Site
Amsterdam
uniQure Investigative Site
Groningen
uniQure Investigative Site
Rotterdam
uniQure Investigative Site
Utrecht
Germany2 sites
uniQure Investigative Site
Berlin
uniQure Investigative Site
Frankfurt
About this study
Official title: A Phase I/II, Open-label, Uncontrolled, Single-dose, Dose-ascending, Multi-centre Trial Investigating an Adeno-associated Viral Vector Containing a Codon-optimized Human Factor IX Gene (AAV5-hFIX) Administered to Adult Patients With Severe or Moderately Severe Hemophilia B
This study evaluates how safe gene therapy treatment with AAV5-hFIX is in adult patients with severe or moderately severe hemophilia B and severe bleeding type.
- Conditions
- Hemophilia B
- Being tested
- AAV5-hFIX
- Keywords
- Hemophilia B, gene therapy
- Medical subject headings
- Hemophilia B
What participants receive
What participants receive. In a randomised study each person is assigned to one group by chance.
AAV5-hFIXGenetic
Also called AAV5 containing a codon-optimized human factor IX gene
AAV5hFIX gene therapy
| Study group | Role | What they receive |
|---|---|---|
| Cohort 1 | Experimental | AAV5-hFIX 5 × 10E12 gc/kg intravenous single infusion Receives: Genetic: AAV5-hFIX |
| Cohort 2 | Experimental | AAV5-hFIX 2 × 10E13 gc/kg intravenous single infusion Receives: Genetic: AAV5-hFIX |
What is being measured
The primary outcome is the main question the study is designed to answer.
Number of Participants With Adverse Events
Measured: From AMT-060 infusion through end of study (5 years post-dose)
Secondary outcomes (11)
FIX-replacement-therapy-free FIX Activity
FIX activity measured any time from 72 hours after latest FIX replacement therapy administration and until next administration of FIX replacement therapy. Only assessments performed more than 10 days after most recent FIX-replacement therapy administration included.
Measured: From AMT-060 infusion through end of study (5 years post-dose)
Total Annualized Bleeding Rate (ABR)
Annualized: Sum of post-treatment bleeding episodes divided by subjects' average number of years (365.25 days) from treatment start to until the data cutoff date.
Measured: From AMT-060 infusion through end of study (5 years post-dose)
Total Consumption of FIX Replacement Therapy
Measured: From AMT-060 infusion through end of study (5 years post dose).
Change From Baseline in Short Form-36 (SF-36) Quality of Life (QoL) Scores
Scores range from 0 to 100, with a higher score defining a more favorable health state.
Measured: From AMT-060 infusion through the end of study (5 years post dose)
Time to Vector DNA Stopped Shedding From Blood, Nasal Secretions, Saliva, Urine, Feces, and Semen
Measured: From AMT-060 infusion through end of study (5 years post dose).
Number of Subjects Developing Neutralizing Antibodies to AAV5
Measured: From AMT-060 infusion through end of study (5 years post dose)
Total IgG and IgM Antibody Titers to AAV5
For subjects with a titer of 109350 and 50, the actual titer is >109350 and <50.
Measured: AMT-060 infusion through end of study (5 years post dose)
Number of Subjects With a Positive AAV5 Capsid-specific T Cell Response
Specific AAV5 response (results >17 SFC/million PBMCs) were regarded as positive.
Measured: From AMT-060 infusion through 26 weeks post-dose
Number of Subjects With Antibodies to FIX
Measured: From AMT-060 infusion through the end of study (5 years post dose)
Number of Subjects With FIX Inhibitors
Measured: From AMT-060 infusion through the end of study (5 years post dose)
Number of Subjects With Clinically Significant Inflammatory Markers: IL-1β, IL-2, IL-6, INFγ, MCP-1
Measured: From AMT-060 infusion through 18 weeks post dose
Timeline
From the start of the study to its completion; the mark is today. Estimated dates are the sponsor’s plan.
- First posted24 Mar 2015 (estimated)
- Study start10 Jun 2015
- Primary completion15 Apr 2021
- Study completion15 Apr 2021
Resources
- Official record on ClinicalTrials.govThe registry entry this page is built from, with its full change history.
- Posted resultsParticipant flow, outcome measures and adverse events reported by the sponsor.
- Publications (1)Papers the sponsor has linked to this study.
- Other trials for Hemophilia BStudies of the same condition, open and under way.
- More trials run by CSL BehringThe sponsor's other registered studies.
- What the trial phases meanHow a treatment moves from first tests in people to approval.
More details
For doctors and researchers: how the study is designed, who runs it, and its registry IDs.
Study design
- Study type
- Interventional
- Phase
- Phase 1/2
- Primary purpose
- Treatment
- Allocation
- Non-randomised
- Intervention model
- Sequential
- Masking
- None (open label)
- Enrolment
- 10 participants (actual)
Sponsor and investigators
- Lead sponsor
- CSL Behring
- Sponsor type
- Industry (pharma, biotech, devices)
- Responsible party
- Sponsor
- Investigators
- uniQure Clinical Trials, Study director, UniQure Biopharma B.V.
IDs, dates and publications
- ClinicalTrials.gov ID
- NCT02396342
- Sponsor's protocol ID
- CT-AMT-060-01
- Status last verified
- Jun 2022
- First submitted
- 4 Mar 2015
- Last updated
- 27 Jun 2022
- Results posted
- Yes, on ClinicalTrials.gov
- Data monitoring committee
- Yes
- Individual data sharing
- No
Publications
Miesbach W, Meijer K, Coppens M, Kampmann P, Klamroth R, Schutgens R, Tangelder M, Castaman G, Schwable J, Bonig H, Seifried E, Cattaneo F, Meyer C, Leebeek FWG. Gene therapy with adeno-associated virus vector 5-human factor IX in adults with hemophilia B. Blood. 2018 Mar 1;131(9):1022-1031. doi: 10.1182/blood-2017-09-804419. Epub 2017 Dec 15.
PubMed 29246900
Study at a glance
From the registry record, last updated by the sponsor on 27 Jun 2022. Recruitment status is as the sponsor reported it: confirm with the study team.
- Official title
- A Phase I/II, Open-label, Uncontrolled, Single-dose, Dose-ascending, Multi-centre Trial Investigating an Adeno-associated Viral Vector Containing a Codon-optimized Human Factor IX Gene (AAV5-hFIX) Administered to Adult Patients With Severe or Moderately Severe Hemophilia B
- ClinicalTrials.gov ID
- NCT02396342
- Acronym / sponsor ID
- CT-AMT-060-01
- Conditions
- Hemophilia B
- Keywords
- Hemophilia B, gene therapy
- Phase
- Phase 1/2
- Study type
- Interventional
- Recruitment status
- Completed
- Enrolment
- 10 participants (actual)
- Lead sponsor
- CSL BehringIndustry (pharma, biotech, devices)
- Study start
- 10 Jun 2015 (actual)
- Primary completion
- 15 Apr 2021 (actual)
- Study completion
- 15 Apr 2021 (actual)
- First posted
- 24 Mar 2015 (estimated)
- Results
- Posted 27 Jun 2022
Clinical summary
The research question as the sponsor registered it. This describes what the study plans to test, not what it found.
This study evaluates how safe gene therapy treatment with AAV5-hFIX is in adult patients with severe or moderately severe hemophilia B and severe bleeding type.
Study design
- Primary purpose
- Treatment
- Allocation
- Non-randomised
- Intervention model
- Sequential
- Masking
- None (open label)
- Number of arms
- 2
| Arm | Type | Receives |
|---|---|---|
| Cohort 1 | Experimental | Genetic: AAV5-hFIXAAV5-hFIX 5 × 10E12 gc/kg intravenous single infusion |
| Cohort 2 | Experimental | Genetic: AAV5-hFIXAAV5-hFIX 2 × 10E13 gc/kg intravenous single infusion |
Who may qualify
- Ages
- 18 years and older
- Sex
- Male only
- Healthy volunteers
- Not accepted
- Age groups
- Adult, Older adult
Key inclusion criteria (12 listed)
- Male
- Age ≥ 18 years
- Patients with congenital hemophilia B classified as one of the following:
- More than 150 previous exposure days of treatment with FIX protein.
- Acceptance to use a condom during sexual intercourse in the period from Investigational Medicinal Product (IMP) administration until AAV5 has been cleared from semen, as evidenced by the central laboratory from negative analysis results for at least 3 consecutively collected semen samples (this criterion is applicable also for subjects who are surgically sterilized)
Key exclusion criteria (24 listed)
- History of FIX inhibitors measured to be ≥ 0.6 Bethesda Units (BU)/mL
- FIX inhibitors ≥ 0.6 BU/mL at Visit 1 (measured by the local laboratory)
- Neutralizing antibodies against AAV5 at Visit 1 (measured by the central laboratory)
- Visit 1 laboratory values (measured by the central laboratory):
- Positive HIV serological test at Visit 1, not controlled with anti-viral therapy as shown by cluster of differentiation 4+ counts ≤ 200 per μL or by a viral load of >200 copies per mL (measured by the central laboratory)
Eligibility is decided by the study team after screening; this overview does not establish that a patient qualifies. Full inclusion and exclusion criteria.
Interventions
| Intervention | Type | Arms |
|---|---|---|
| AAV5-hFIXAlso: AAV5 containing a codon-optimized human factor IX geneAAV5hFIX gene therapy | Genetic | Cohort 1, Cohort 2 |
Primary outcome
Number of Participants With Adverse Events
Time frame: From AMT-060 infusion through end of study (5 years post-dose)
11 secondary outcomes
FIX-replacement-therapy-free FIX Activity
Time frame: From AMT-060 infusion through end of study (5 years post-dose)
Total Annualized Bleeding Rate (ABR)
Time frame: From AMT-060 infusion through end of study (5 years post-dose)
Total Consumption of FIX Replacement Therapy
Time frame: From AMT-060 infusion through end of study (5 years post dose).
Change From Baseline in Short Form-36 (SF-36) Quality of Life (QoL) Scores
Time frame: From AMT-060 infusion through the end of study (5 years post dose)
Time to Vector DNA Stopped Shedding From Blood, Nasal Secretions, Saliva, Urine, Feces, and Semen
Time frame: From AMT-060 infusion through end of study (5 years post dose).
Number of Subjects Developing Neutralizing Antibodies to AAV5
Time frame: From AMT-060 infusion through end of study (5 years post dose)
Total IgG and IgM Antibody Titers to AAV5
Time frame: AMT-060 infusion through end of study (5 years post dose)
Number of Subjects With a Positive AAV5 Capsid-specific T Cell Response
Time frame: From AMT-060 infusion through 26 weeks post-dose
Number of Subjects With Antibodies to FIX
Time frame: From AMT-060 infusion through the end of study (5 years post dose)
Number of Subjects With FIX Inhibitors
Time frame: From AMT-060 infusion through the end of study (5 years post dose)
Number of Subjects With Clinically Significant Inflammatory Markers: IL-1β, IL-2, IL-6, INFγ, MCP-1
Time frame: From AMT-060 infusion through 18 weeks post dose
Results and safety
Loading the posted results from ClinicalTrials.gov…
Research links
- Official record on ClinicalTrials.govLast updated by the sponsor 27 Jun 2022.
- Posted resultsParticipant flow, baseline, all outcome measures and adverse events.
- Derived from this study: PubMed 29246900Miesbach W, Meijer K, Coppens M, Kampmann P, Klamroth R, Schutgens R, Tangelder M, Castaman G, Schwable J, Bonig H, Seifried E, Cattaneo F, Meyer C, Leebeek FWG. Gene therapy with adeno-associated virus vector 5-human factor IX in adults with hemophilia B. Blood. 2018 Mar 1;131(9):1022-1031. doi: 10.1182/blood-2017-09-804419. Epub 2017 Dec 15.
- Individual participant dataSharing planned: No
Related trials for Hemophilia B
Active, not recruitingObservational study
A Study to Learn About the Study Medicine -Hympavzi in Congenital Hemophilia Patients Without Inhibitors in Japan.
Hemophilia A or B
Active, not recruitingPhase 3
A Study to Evaluate the Efficacy and Safety of Factor IX Gene Therapy With PF-06838435 in Adult Males With Moderately Severe to Severe Hemophilia B
Hemophilia B
Not yet recruiting
Safety of Intraosseous Anaesthesia in Children With Haemophilia
Haemophilia A, Haemophilia B
Not yet recruitingPhase 1
Lentiviral FIX Gene Therapy
Hemophilia B
RecruitingPhase 3
A Study to Investigate the Efficacy and Safety of Fitusiran Prophylaxis in Male Participants Aged 1 to Less Than 12 Years With Hemophilia A or B
Hemophilia
Referral and contact
AzTrials does not enrol participants or take referrals. Contact the study team or a site listed below; they decide who can take part. This study is not recruiting at the moment.
uniQure Clinical Trials study director
UniQure Biopharma B.V.
7 sites in 3 countries: see every site and its status.
Questions about this trial
What is this clinical trial studying?
A Phase 1/2 study testing AAV5-hFIX in people with Hemophilia B, run by CSL Behring at 7 sites in 3 countries.
The full registered description is in the About this study section and the official record.
Who may be eligible to take part?
The sponsor lists 12 inclusion and 24 exclusion criteria. Eligibility is decided by the study team after screening, so read the full criteria and contact a listed site.
Is this clinical trial currently recruiting?
The record says: finished, as of the sponsor's last update on 27 Jun 2022. Status can change between updates, so confirm with the study contact before making plans.
Where is the study taking place?
The record lists 7 sites in Netherlands, Germany, Denmark. Whether a site is taking part right now should be confirmed with that site. See every site.
What are the possible benefits and risks?
They depend on the study and the treatment, and no study can promise a benefit. The study team explains the known risks during informed consent, before anyone joins; the record itself does not list them.
What does this combined phase mean?
Phase 1 studies test a treatment in a small group of people for the first time or in a new way, mainly to check safety and find the right dose.
Phase 2 studies give the treatment to a larger group to see whether it has the intended effect and to keep checking safety.
Not every study follows the same path, and some studies (observational studies, device studies) have no phase.
Are results available for this study?
Yes. Results are posted in the registry (first posted 27 Jun 2022). A summary is in the For doctors view, and the full results are on ClinicalTrials.gov.
How can a doctor refer a patient or contact the research team?
The record lists no contact. The official record names the sponsor, who can be asked directly. AzTrials does not enrol participants or take referrals.
What does the primary outcome measure?
Number of Participants With Adverse Events (time frame: From AMT-060 infusion through end of study (5 years post-dose)). It is what the study was designed to measure, not a finding.
Where can I read the original study information?
On the ClinicalTrials.gov record for NCT02396342, which also lists 1 linked publication.
Does a listing mean the treatment is approved or proven to work?
No. A listing means the study is registered. It does not show that the treatment is safe, works, or is approved by a regulator.
How often is this information updated?
AzTrials copies changed records from ClinicalTrials.gov every night and reloads the whole registry every week. The sponsor last updated this record on 27 Jun 2022.